Trilogy of Fallot

Trilogy of Fallot
Classification and external resources
Specialty	medical genetics
ICD-10	Q21.3 ICD9 = 746.09, 746.8 (CDC/BPA 746.84)
MeSH	D014286

The trilogy of Fallot is a congenital heart disease consisting of the following defects: pulmonary valve stenosis, right ventricular hypertrophy and atrial septal defect. This disease is 1.6-1.8% of all congenital heart defects.

Mechanism

It consists of the following:

The first two of these are also found in the tetralogy of Fallot. However, the tetralogy has a ventricular septal defect instead of an atrial one, and it also involves an overriding aorta.

Treatment

Thoracotomy is used to surgically correct this pathology.^[1]

History

It is named in honor of its discoverer: Etienne Fallot.^[2]

References

↑ Wang YQ, Chen RK, Ye WW, et al. (1999). "Open-heart surgery in 48 patients via a small right anterolateral thoracotomy". Tex Heart Inst J. 26 (2): 124–8. PMC 325616 . PMID 10397435.
↑ synd/2283 at Who Named It?

Congenital heart defects (Q20–Q24, 745–746)

Cardiac shunt/
heart septal defect

Aortopulmonary septal defect	R→L: Double outlet right ventricle Taussig–Bing syndrome Transposition of the great vessels dextro levo Persistent truncus arteriosus Aortopulmonary window
Atrial septal defect	L→R: Sinus venosus atrial septal defect Lutembacher's syndrome
Ventricular septal defect	L→R and R→L: Eisenmenger's syndrome R→L, with other conditions: Tetralogy of Fallot
Atrioventricular septal defect	L→R: Ostium primum

Valvular heart disease/
heart chambers

Right	pulmonary valves stenosis insufficiency tricuspid valves stenosis atresia Ebstein's anomaly Hypoplastic right heart syndrome Uhl anomaly
Left	aortic valves stenosis insufficiency bicuspid mitral valves stenosis regurgitation Hypoplastic left heart syndrome

Other

This article is issued from Wikipedia. The text is licensed under Creative Commons - Attribution - Sharealike. Additional terms may apply for the media files.