Thymidine kinase 2, mitochondrial

TK2
Identifiers
AliasesTK2, MTDPS2, MTTK, SCA31, thymidine kinase 2, mitochondrial, PEOB3
External IDsMGI: 1913266 HomoloGene: 3392 GeneCards: TK2
Gene location (Human)
Chr.Chromosome 16 (human)[1]
BandNo data availableStart66,508,003 bp[1]
End66,552,544 bp[1]
Orthologs
SpeciesHumanMouse
Entrez

7084

57813

Ensembl

ENSG00000166548

ENSMUSG00000035824

UniProt

O00142

Q9R088

RefSeq (mRNA)

NM_021028

RefSeq (protein)

n/a

Location (UCSC)Chr 16: 66.51 – 66.55 MbChr 16: 104.23 – 104.25 Mb
PubMed search[3][4]
Wikidata
View/Edit HumanView/Edit Mouse

Thymidine kinase 2, mitochondrial is a protein that in humans is encoded by the TK2 gene. [5]

Function

This gene encodes a deoxyribonucleoside kinase that specifically phosphorylates thymidine, deoxycytidine, and deoxyuridine. The encoded enzyme localizes to the mitochondria and is required for mitochondrial DNA synthesis. Mutations in this gene are associated with a myopathic form of mitochondrial DNA depletion syndrome. Alternate splicing results in multiple transcript variants encoding distinct isoforms, some of which lack transit peptide, so are not localized to mitochondria.

References

Further reading

This article incorporates text from the United States National Library of Medicine, which is in the public domain.


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