IgA pemphigus
| IgA pemphigus | |
|---|---|
| Classification and external resources | |
| eMedicine | article/1063776 |
IgA pemphigus is a subtype of pemphigus with two distinct forms:
- Subcorneal pustular dermatosis (also known as Sneddon–Wilkinson disease and pustulosis subcornealis)[1] is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils.[2][3]:203 This is distinct from and not to be confused with subcorneal pustular dermatosis type of IgA pemphigus. Sneddon's syndrome, also known as Ehrmann-Sneddon syndrome, is also a different syndrome.[4]
- Intraepidermal neutrophilic IgA dermatosis is characterized histologically by intraepidermal bullae with neutrophils, some eosinophils, and acantholysis.[3]:465
See also
- Pemphigus
- List of cutaneous conditions
- List of conditions caused by problems with junctional proteins
- List of immunofluorescence findings for autoimmune bullous conditions
References
- ↑ RESERVED, INSERM US14 -- ALL RIGHTS. "Orphanet: Subcorneal pustular dermatosis". www.orpha.net. Retrieved 8 March 2017.
- ↑ Irwin M. Freedberg; et al., eds. (2003). Fitzpatrick's dermatology in general medicine. (6th ed.). New York, NY [u.a.]: McGraw-Hill. p. 625. ISBN 0-07-138076-0.
- 1 2 James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0-7216-2921-0.
- ↑ Berlit, Peter. "Sneddon's Syndrome". Orphanet.
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