Glycerol phenylbutyrate

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Systematic (IUPAC) name
1,2,3-Propanetriyl tris(4-phenylbutanoate)
Clinical data
Trade names	Ravicti
AHFS/Drugs.com	entry
Pregnancy cat.	C (US)
Legal status	℞-only (US)
Routes	Oral
Identifiers
CAS number	611168-24-2
ATC code	A16AX09
PubChem	CID 10482134
DrugBank	DB08909
ChemSpider	8657541
ChEMBL	CHEMBL2105745
Chemical data
Formula	C₃₃H₃₈O₆
Mol. mass	530.651 g/mol
SMILES C1=CC=C(C=C1)CCCC(=O)OCC(COC(=O)CCCC2=CC=CC=C2)OC(=O)CCCC3=CC=CC=C3
InChI InChI=1S/C33H38O6/c34-31(22-10-19-27-13-4-1-5-14-27)37-25-30(39-33(36)24-12-21-29-17-8-3-9-18-29)26-38-32(35)23-11-20-28-15-6-2-7-16-28/h1-9,13-18,30H,10-12,19-26H2 Key:ZSDBFLMJVAGKOU-UHFFFAOYSA-N

Glycerol phenylbutyrate (USAN), trade name Ravicti, is a medication used in the treatment of certain inborn urea cycle disorders. The medication works by preventing the harmful build up of ammonia in the body.^[1]

References

↑ http://www.fda.gov/NewsEvents/Newsroom/PressAnnouncements/ucm337639.htm

Other alimentary tract and metabolism products (A16)

Amino acids and derivatives

Levocarnitine
Ademetionine
Levoglutamide
Cysteamine
Carglumic acid
Betaine

Enzymes

Carbohydrate metabolism: sucrase (Sacrosidase)
alpha-glucosidase (Alglucosidase alfa)

Glycolipid/sphingolipid: glucocerebrosidase (Alglucerase
Imiglucerase
Taliglucerase alfa
Velaglucerase alfa)
alpha-galactosidase (Agalsidase alfa
Agalsidase beta)

Glycosaminoglycan: iduronidase (Laronidase)
arylsulfatase B (Galsulfase)
iduronate-2-sulfatase (Idursulfase)

Various alimentary tract
and metabolism products

M: DIG

anat (t, g, p)/phys/devp/enzy

noco/cong/tumr, sysi/epon

proc, drug (A2A/2B/3/4/5/6/7/14/16), blte

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