| Polysplenia | |
|---|---|
| Classification and external resources | |
| ICD-10 | Q89.0 |
| ICD-9 | 759.0 |
| DiseasesDB | 32864 |
| eMedicine | ped/2514 |
Polysplenia is a congenital disease manifested by multiple small accessory spleens.[1]
There are frequent associated congenital anomalies all related to deviations in the development of anatomical asymmetries in early embryonic stages. These conditions considered together are called "polysplenia syndrome".[2]
Associated conditions include heterotaxy syndrome, intestinal malrotation, situs inversus, biliary atresia, and the range of congenital cardiac malformations.
Although present, the multiple small spleens are ineffective; this is termed functional asplenia.
|
|||||||||||||||||