ARTS-1

Type 1 tumor necrosis factor receptor shedding aminopeptidase regulator

Crystal structure of the open state of human endoplasmic reticulum aminopeptidase 1 ERAP1.[1]
Identifiers
Symbols ARTS-1; A-LAP; ALAP; APPILS; ARTS1; ERAAP; ERAP1; KIAA0525; PILSAP
External IDs OMIM606832 MGI1933403 HomoloGene56754 GeneCards: ARTS-1 Gene
RNA expression pattern
More reference expression data
Orthologs
Species Human Mouse
Entrez 51752 80898
Ensembl ENSG00000164307 ENSMUSG00000021583
UniProt Q9NZ08 Q6GTP5
RefSeq (mRNA) NM_001040458 NM_030711
RefSeq (protein) NP_001035548 NP_109636
Location (UCSC) Chr 5:
96.12 – 96.17 Mb
Chr 13:
75.11 – 75.16 Mb
PubMed search [1] [2]

Type 1 tumor necrosis factor receptor shedding aminopeptidase regulator, also known as ARTS-1, is a protein which in humans is encoded by the ARTS-1 gene.[2]

ARTS1 is also known as:

Endoplasmic reticulum aminopeptidase 1 is active in the endoplasmic reticulum, which is involved in protein processing and transport. This protein is an aminopeptidase, which is an enzyme that cleaves other proteins into smaller fragments called peptides.

ERAP1 has two major functions in the immune system:

Contents

Function

ARTS-1 is a member of the M1 family of zinc metallopeptidases which acts as a aminopeptidase that degrades oligopeptides by cleavage starting at the amino terminus. One of the functions of aminopeptidases is to degrade potentially toxic peptides in the cytosol.[2]

ARTS-1 is a transmembrane protein that is localized to the endoplasmic reticulum. It has been implicated in the following functions:

Clinical significance

Aminopeptidases play a role in the metabolism of several peptides that may be involved in blood pressure and the pathogenesis of essential hypertension.[2] Mutations in the ARTS-1 have been linked to an increased risk of ankylosing spondylitis.[4]

The protein encoded by this gene is an aminopeptidase involved in trimming HLA class I-binding precursors so that they can be presented on MHC class I molecules. The encoded protein acts as a monomer or as a heterodimer with ERAP2. This protein may also be involved in blood pressure regulation by inactivation of angiotensin II. Three transcript variants encoding two different isoforms have been found for this gene.[2]

References

Further reading