Taussig-Bing syndrome

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Taussig-Bing syndrome Classification and external resources
ICD-10	Q20.1
ICD-9	745.11
OMIM	217095
DiseasesDB	32215
eMedicine	ped/2509  ped/2508
MeSH	D004310

Taussig-Bing syndrome is a cyanotic congenital heart defect (CHD) in which the patient has both double outlet right ventricle (DORV) and subpulmonic ventricular septal defect (VSD).

In DORV, instead of the normal situation where blood from the left ventricle (LV) flows out to the aorta and blood from the right ventricle (RV) flows out to the pulmonary artery, both aorta and pulmonary artery are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is subpulmonic (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.

The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of dextro-Transposition of the great arteries (but the surgical repair is different).

v • d • e Congenital malformations and deformations of circulatory system (Q20-Q28, 745-747) Cardiac chambers and connections Persistent truncus arteriosus - Double outlet right ventricle (Taussig-Bing syndrome) - Transposition of the great vessels (dextro, levo) Cardiac septa Ventricular septal defect - Atrial septal defect (Lutembacher's syndrome) - Atrioventricular septal defect (Ostium primum) - Tetralogy of Fallot - Eisenmenger's syndrome Valvular heart disease/ heart chambers Right: pulmonary and tricuspid valves pulmonary valves (stenosis, insufficiency) - tricuspid valves (stenosis, atresia) - Ebstein's anomaly Left: aortic and mitral valves aortic valves (stenosis, insufficiency, bicuspid) - mitral valves (stenosis, regurgitation) - Hypoplastic left heart syndrome Other congenital malformations of heart Dextrocardia - Levocardia - Cor triatriatum Vascular malformation Great arteries aorta: Patent ductus arteriosus - Aortic coarctation - Interrupted aortic arch - Overriding aorta - Aneurysm of sinus of Valsalva - Vascular ring pulmonary artery: Pulmonary atresia Great veins superior vena cava: Persistent left superior vena cava pulmonary vein: Total anomalous pulmonary venous connection - Scimitar syndrome Other Arteriovenous malformation (Cerebral arteriovenous malformation) See also non-congenital conditions (I, 390-459)