Polysplenia

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Polysplenia is a congenital disease manifested by multiple small accessory spleens. There are frequent associated congental anomalies all related to deviations in the development of anatomical asymmetries in early embryonic stages. Associated conditions include heterotaxy syndrome, intestinal malrotation, situs inversus, biliary atresia, and the range of congenital cardiac malformations.

Although present, the multiple small spleens are ineffective; this is termed functional asplenia.