Mondini Dysplasia
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Mondini Dysplasia, sometimes known as a Mondini malformation, is an abnormality in the inner ear that can be the cause of hearing loss.
A person with Mondini dysplasia has a cochlea that is incomplete. A normal cochlea has two and a half turns, a cochlea with Mondina dysplasia has two, one and a half, one, or no turns (or increments, obviously). This results in gradual or even sudden hearing loss that may be profound.
